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Acylcarnitine C10:1 Unit Converter

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Also known as: Decenoylcarnitine, C10:1 Carnitine

Convert Acylcarnitine C10:1

What is Acylcarnitine C10:1?

Acylcarnitine C10:1 (decenoylcarnitine) is a medium-chain unsaturated acylcarnitine formed when decenoic acid (a 10-carbon fatty acid with one double bond) is bound to carnitine for transport into mitochondria.

It reflects the activity of medium-chain fatty acid oxidation, specifically the breakdown of unsaturated medium-chain fats with 6 to 12 carbon atoms. Unlike its saturated counterpart C10 (decanoylcarnitine), C10:1 contains a double bond, making it a distinct intermediate in beta-oxidation.

C10:1 is typically measured as part of an acylcarnitine profile alongside C6, C8, and C10. It serves as a secondary diagnostic marker for medium-chain acyl-CoA dehydrogenase (MCAD) deficiency, one of the most common inherited disorders of fatty acid oxidation.

Where Does Acylcarnitine C10:1 Come From?

Decenoylcarnitine is produced in the liver and skeletal muscle when unsaturated medium-chain fatty acids are conjugated with carnitine for transport into mitochondria during beta-oxidation.

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